Extralobar congenital pulmonary sequestration is a rare congenital malformation in which a portion of the lung is not connected to the normal airways and is supplied by its own blood supply. It is usually located in the lower part of the chest and is not connected to the trachea or bronchi. It is usually asymptomatic, but can cause recurrent infections, chest pain, and difficulty breathing. Treatment usually involves surgical removal of the affected lobe.

The most common symptoms of Extralobar Congenital Pulmonary Sequestration (EPS) include:

-Persistent cough
-Shortness of breath
-Wheezing
-Recurrent chest infections
-Abdominal pain
-Fever
-Failure to thrive
-Rapid breathing
-Rapid heart rate
-Bluish discoloration of the skin (cyanosis)
-Clubbing of the fingers and toes
-Enlarged liver and spleen (hepatosplenomegaly)

The exact cause of extralobar congenital pulmonary sequestration is unknown. It is thought to be caused by abnormal development of the fetal lungs during the early stages of pregnancy. It is believed that the abnormal development of the fetal lungs is due to a combination of genetic and environmental factors.

The primary treatment for extralobar congenital pulmonary sequestration is surgical resection. This involves removing the sequestered lung tissue and any associated blood vessels. In some cases, a portion of the diaphragm may also need to be removed. In some cases, a minimally invasive approach may be used, such as video-assisted thoracoscopic surgery (VATS). In some cases, a combination of surgery and chemotherapy may be used. In some cases, radiation therapy may be used to shrink the sequestered tissue before surgery.

1. Low birth weight
2. Premature birth
3. Congenital heart defects
4. Abnormalities of the diaphragm
5. Abnormalities of the chest wall
6. Abnormalities of the abdominal wall
7. Abnormalities of the gastrointestinal tract
8. Abnormalities of the genitourinary tract
9. Chromosomal abnormalities
10. Family history of congenital pulmonary sequestration

At this time, there is no cure for extralobar congenital pulmonary sequestration. Treatment typically involves surgical removal of the sequestered lung tissue. In some cases, medications may be prescribed to help manage symptoms such as pain or infection.