Desmoplastic small round cell tumor (DSRCT) is a rare type of cancer that usually affects young males. It is a type of sarcoma, which is a cancer that develops in the body's connective tissues. DSRCT is a fast-growing tumor that typically starts in the abdomen and can spread to other parts of the body, such as the lungs, liver, and lymph nodes. Treatment typically involves surgery, chemotherapy, and radiation.

The most common symptoms of Desmoplastic Small Round Cell Tumor (DSRCT) include abdominal pain, abdominal swelling, and a mass in the abdomen. Other symptoms may include nausea, vomiting, constipation, and weight loss. In some cases, the tumor may spread to other parts of the body, such as the lungs, liver, and lymph nodes, which can cause additional symptoms.

The exact cause of desmoplastic small round cell tumor (DSRCT) is unknown. However, it is believed to be caused by a genetic mutation that occurs in the cells of the body. This mutation causes the cells to grow and divide abnormally, leading to the formation of the tumor.

The treatment for desmoplastic small round cell tumor (DSRCT) typically involves a combination of surgery, chemotherapy, and radiation therapy. Surgery is used to remove as much of the tumor as possible. Chemotherapy is used to kill any remaining cancer cells. Radiation therapy is used to shrink the tumor and reduce the risk of recurrence. In some cases, targeted therapies such as immunotherapy may also be used.

1. Male gender
2. Young age (typically diagnosed in adolescents and young adults)
3. Exposure to radiation
4. Genetic mutations in the DSRCT1 gene
5. Family history of the disease

At this time, there is no known cure for desmoplastic small round cell tumor (DSRCT). Treatment typically involves a combination of chemotherapy, radiation therapy, and surgery. Medications used to treat DSRCT may include cisplatin, doxorubicin, etoposide, ifosfamide, and vincristine.